Brain involvement in Wegener's granulomatosis. Case report
Keywords:
Wegener's granulomatosis, central nervous system, cerebral vasculitis, case reportsAbstract
The granulomatosis with polyangiitis (GPA), known before as Wegener's granulomatosis, is an autoimmune multisystemic disease, not so common, of unknown etiology. The compromise of this particular disease to the neurological central system is very rare although it’s very important because of its relationship with refractory disease periods.
The differential diagnosis of the manifestations of the GPA at cerebral level it’s not easy to see because there are not that allows the exclusion of other lesions intra or extra axials.
We present the case of the patient with Wegener granulomatosis of long evolution that begins with seizures and motor deficit secondary to a left parietal intra axial mass. The clinical characteristics histopathological and radiological are careful described and the role of surgery in management is discussed.
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Copyright (c) 2016 José Leonardo Acosta Quintana, Christian Xavier Diez Pingel, María Lorena Acosta García, Salomé Álvarez
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