Multiple endocrine neoplasia type 1 About a case
Keywords:
multiple endocrine neoplasia, NEM1, Zollinger Ellison syndrome, adenohypophysis, pancreatic islets, parathyroidAbstract
Multiple endocrine neoplasia type 1 (MEN1) is a rare autosomal dominant hereditary syndrome, classically characterized by the presence of tumors in several glands (parathyroid, anterior pituitary and pancreatic islets)12
The prevalence of MEN 1 is approximately 2 per 100,000 inhabitants.11
The Zollinger Ellison syndrome (ZES) is one of the three neoplasias that form part of the MEN 1, and corresponds to 20 to 60%.1
The clinical case of a 66-year-old male patient, with a clinical of Zollinger Ellison Syndrome, who in a subsequent investigation shows functional abnormality of the parathyroid glands, fulfilling diagnostic criteria of Multiple Endocrine Neoplasia type 1 (NEM1)
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Copyright (c) 2016 Roberto Barreno, Verónica Ayala, Isabel Guamán, Nestor Basantes, Edgar Changoluisa, Margarita del Rocío Montes Moreno
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